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Tay Sachs






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Tay Sachs

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(Medicine) genetic disorder of lipid metabolism; hereditary disorder caused by deficiency of a vital enzyme called Hexosaminidase (occurs in east European Jewish families); lipids accumulation that affects the brain and nervous tissues resulting in death in early childhood

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Tay Sachs

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n. Tay Sachs, (Medizin) genetische Fehlfunktion des lipiden Metabolismus; vererbte Krankheit durch den Mangel an vitalen Enzymen (Hexosarnindase) verursacht (kommt bei jüdischen Familien askenasischer Herkunft vor); lipide Akkumulation die das Gehirn und Nervengewebe angreift und Tod in früher Kindheit verursacht

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